Status epilepticus in a case with wilson's disease during D-pencillamine treatment.

We report on a case of Wilson’s disease in a young male presenting with status epilepticus during D-pencillamine treatment. The patient was admitted to our neurogical clinic for status epilepticus and was successfully treated with antiepileptic drugs. He had been on regular D-pencillamine treatment for three years. Magnetic resonance imaging showed lesions bilaterally in subcortical areas of frontal lobes, putamen, thalamus, globus pallidum and caudate nuclei. Wilson’s disease had been diagnosed. Few patients with Wilson’s disease presenting with epilepsy and status epilepticus have been reported. Although the patient had received D-pencillamine treatment, the diagnosis of Wilson’s disease should be considered in patients who present with status epilepticus.